The New Indian Journal of OBGYN. 10(2):439-441

Pregnancy with Ebstein anomaly and early onset severe preeclampsia - a rare case

Tajinder Kaur, Purnima Surabhi, Mehroz Ahmed Mirza

ABSTRACT

Ebstein anomaly is a rare congenital cardiac abnormality, with a prevalence of 5.2 per 100,000 live births and accounts for 1% of congenital heart defects. The specific defect involves the abnormal attachment of tricuspid valve leaflets to the valve annulus, with displacement of septal and posterior leaflets, leading to downward displacement of effective orifice and division of right ventricle into two portions. The common cardiac lesions associated with Ebstein anomaly are ASD, PFO and WPW syndrome. We present a case of pregnancy with Ebstein anomaly (diagnosed at our hospital, with preeclampsia, resulting in preterm caesarean delivery. The patient had no complications and tolerated surgery, neonatal outcome was SGA (small for gestational age) birth. The pregnancy is safe in woman with Ebstein anomaly, who don’t develop cyanosis or heart failure, and vaginal delivery is preferred. Preterm birth and SGA births are common in pregnancy with Ebstein anomaly. A close observation is required if mother develops cyanosis or arrhythmias.